Interventional closure of RPA-to-LA communication in an oligosymptomatic neonate

Benz, Dominik ; Burkhardt, Barbara ; Quandt, Daniel ; Stambach, Dominik ; Knirsch, Walter ; Kretschmar, Oliver

In: European Journal of Pediatrics, 2014, vol. 173, no. 12, p. 1703-1705

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    Summary
    Direct communication between the right pulmonary artery (RPA) and the left atrium (LA) is a very rare cardiac malformation. Clinical presentation of RPA-to-LA communication depends on the size of the communication, the amount of right-to-left shunt, the patient's age, and pulmonary vascular resistance. Patients with small communications usually present oligosymptomatic and are diagnosed at an older age. A delay of diagnosis bears the risk of severe complications and needs to be prevented by proper work-up of oligosymptomatic neonates. Treatment of RPA-to-LA communications used to be performed by surgical closure, and the interventional approach has only been established as a less invasive alternative in recent years. Conclusion: Although patients with small RPA-to-LA communications usually present oligosymptomatic, early diagnosis and treatment is essential to prevent life-threatening complications.